Prune Belly Syndrome
نویسندگان
چکیده
Prune belly syndrome is a rare congenital disorder of the urinary system, characterized by a triad of abnormalities. The aetiology is not known. Many infants are either stillborn or die within the first few weeks of life from severe lung or kidney problems, or a combination of congenital anomalies.
منابع مشابه
Concurrence of prune belly syndrome with meningomyelocele
Prune Belly Syndrome (PBS) comprises a triad of abdominal wall deficiency, urogenital abnormalities and cryptorchidism. Neurologic abnormalities are unusual in prune belly syndrome. Here, we report a rare association of meningomyelocele with prune belly syndrome and provide an embryologic perspective to this concurrence.
متن کاملPrune Belly Syndrome in Adolescence: A Case Report
The Prune Belly syndrome also known as Eagle Barret syndrome is a rare disorder. We report a rare case of Prune Belly syndrome in 17 year old boy. Patient presented with complains of absence of both testis in scrotum since birth. On examination patient was found to have lax abdominal wall. Patient was further evaluated and found to have shrunken small right kidney and left hydroureteronephrosis...
متن کاملIt's not All Doom and Gloom: Prune Belly Syndrome Associated with VACTERL
Prune belly syndrome is a rare abnormality; its association with VACTERL is even rarer. This association has been reported in literature a few times since first reported in 1993 and so far the majority have either been stillbirths or died shortly after birth. We present a case of Prune belly syndrome associated with VACTERL who is now one year old.
متن کاملStructural study of gubernaculum testis in fetuses with prune belly syndrome.
PURPOSE We compared and contrasted the structure of the gubernaculum testis in fetuses with prune belly syndrome and normal controls. MATERIALS AND METHODS We studied a total of 6 gubernacula from 3 male fetuses with prune belly syndrome and a total of 14 from 7 male fetuses without an anomaly. Gubernacular specimens were cut into 5 μm sections and stained with Masson trichrome to quantify co...
متن کاملPrune Belly Syndrome: Errors in Management and Complications of Treatment
Prune Belly Syndrome is a condition in which the abdominal wall, urinary tract and testes are affected resulting in a severely curtailed life span. With proper management these patients could have a normal, productive life.
متن کاملPrune-belly syndrome detected by ultrasound in the first trimester and the usefulness of vesicocentesis as a modality of treatment
Prune-belly syndrome may be related to lower urinary tract obstruction (LUTO). LUTO in the early gestational age exacerbates fetal renal function and may require intrauterine intervention. If early developed LUTO causes bladder distension and abdominal musculature deficiency, it will result in prune belly syndrome. Therefore, early detection of the disease and proper treatment before the renal ...
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ورودعنوان ژورنال:
دوره 2011 شماره
صفحات -
تاریخ انتشار 2011